ALDH6A1

Gene Symbol ALDH6A1
Entrez Gene 4329
Alt Symbol MMSADHA, MMSDH
Species Human
Gene Type protein-coding
Description aldehyde dehydrogenase 6 family, member A1
Other Description malonate-semialdehyde dehydrogenase|methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial|mitochondrial acylating methylmalonate-semialdehyde dehydrogenase
Swissprots J3KNU8 B4DFS8 B2R609 Q02252 Q9UKM8
Accessions AAG29581 EAW81158 EAW81159 EAW81160 Q02252 AF038011 AAB92620 AF148505 AAF04489 AF159889 AAF80380 AI244036 AJ249994 CAB76468 AK222687 BAD96407 AK223244 BAD96964 AK294243 BAG57539 AK311478 AK312389 BAG35306 AW418653 BC004909 AAH04909 BC032371 AAH32371 DQ892921 ABM83847 DQ893680 ABM84606 EU176729 ABW03530 M93405 AAA36328 NM_001278593 NP_001265522 NM_001278594 NP_001265523 NM_005589 NP_005580
Function Plays a role in valine and pyrimidine metabolism. Binds fatty acyl-CoA.
Subcellular Location Mitochondrion.
Top Pathways Inositol phosphate metabolism, Carbon metabolism, Valine, leucine and isoleucine degradation, beta-Alanine metabolism, Propanoate metabolism