EHHADH

Gene Symbol EHHADH
Entrez Gene 1962
Alt Symbol ECHD, FRTS3, L-PBE, LBFP, LBP, PBFE
Species Human
Gene Type protein-coding
Description enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase
Other Description 3,2-trans-enoyl-CoA isomerase|L-3-hydroxyacyl-CoA dehydrogenase|L-bifunctional protein, peroxisomal|PBE|enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase|peroxisomal bifunctional enzyme|peroxisomal enoyl-CoA hydratase
Swissprots Q58EZ5 Q08426 A8K6Y3 B4DWG3 D3DNU0
Accessions AAA56760 CAD22483 EAW78228 EAW78229 EAW78230 Q08426 AK223460 BAD97180 AK291798 BAF84487 AK301521 BAG63025 BC011030 BC030982 AAH30982 BC038948 AAH38948 BC110460 AAI10461 DC418722 L07077 AAA53289 S50245 AAB19482 XM_006713525 XP_006713588 XM_011512517 XP_011510819 NM_001166415 NP_001159887 NM_001966 NP_001957
Subcellular Location Peroxisome.
Tissue Specificity Liver and kidney. Strongly expressed in the terminal segments of the proximal tubule. Lower amounts seen in the brain. {ECO:0000269|PubMed:24401050, ECO:0000269|PubMed:8188243}.
Top Pathways Peroxisome, PPAR signaling pathway, Tryptophan metabolism, Fatty acid degradation, Carbon metabolism