SGSH

Gene Symbol SGSH
Entrez Gene 6448
Alt Symbol HSS, MPS3A, SFMD
Species Human
Gene Type protein-coding
Description N-sulfoglucosamine sulfohydrolase
Other Description N-sulphoglucosamine sulphohydrolase|heparan sulfate sulfatase|mucopolysaccharidosis type IIIA|sulfoglucosamine sulfamidase|sulphamidase
Swissprots A8K5E2 P51688
Accessions AAB17952 EAW89590 EAW89591 P51688 AB209900 BAD93137 AK095969 BAG53179 AK222890 BAD96610 AK291257 BAF83946 AK304706 BAH14242 AK309927 AW274014 BC047318 AAH47318 BF445930 DC319407 U30894 AAA86530 XM_005257582 XP_005257639 XM_005257583 XP_005257640 XM_011525126 XP_011523428 XM_011525127 XP_011523429 XR_934532 NM_000199 NP_000190
Subcellular Location Lysosome.
Top Pathways Lysosome, Glycosaminoglycan degradation