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CLN3 Antibody (C-1) is an IgG2b κ mouse monoclonal CLN3 antibody (also designated CLN3 antibody) that detects the CLN3 protein of mouse, rat and human origin by WB, IP, IF and ELISA. CLN3 Antibody (C-1) is available as both the non-conjugated anti-CLN3 antibody form, as well as multiple conjugated forms of anti-CLN3 antibody, including agarose, HRP, PE, FITC and multiple Alexa Fluor® conjugates. CLN3 is a highly glycosylated, hydrophobic, 438-amino acid protein with 6 transmembrane domains. The CLN3 protein localizes to the lysosomal membrane and plays a role in lysosomal function. It may act as a chaperone involved in the folding and unfolding of other proteins, namely subunit C of the ATP synthase complex. Mutations in the CLN3 gene cause Batten disease, a recessively inherited neurodegenerative disorder of childhood caused by lysosomal accumulation of hydrophobic material, mainly ATP synthase subunit C. Batten disease is the most common form of a group of disorders known as neuronal ceroid lipofuscinoses (NCLs). Symptoms of Batten disease include progressive loss of vision, seizures, and psychomotor disturbances.
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Ordering Information
Product Name | Catalog # | UNIT | Price | Qty | FAVORITES | |
CLN3 Antibody (C-1) | sc-398192 | 200 µg/ml | $310.00 | |||
CLN3 Antibody (C-1): m-IgG Fc BP-HRP Bundle | sc-530716 | 200 µg Ab; 10 µg BP | $348.00 | |||
CLN3 Antibody (C-1): m-IgGκ BP-HRP Bundle | sc-524246 | 200 µg Ab, 40 µg BP | $348.00 | |||
CLN3 Antibody (C-1): m-IgG2b BP-HRP Bundle | sc-550217 | 200 µg Ab; 10 µg BP | $348.00 | |||
CLN3 Antibody (C-1) AC | sc-398192 AC | 500 µg/ml, 25% agarose | $408.00 | |||
CLN3 Antibody (C-1) HRP | sc-398192 HRP | 200 µg/ml | $310.00 | |||
CLN3 Antibody (C-1) FITC | sc-398192 FITC | 200 µg/ml | $324.00 | |||
CLN3 Antibody (C-1) PE | sc-398192 PE | 200 µg/ml | $337.00 | |||
CLN3 Antibody (C-1) Alexa Fluor® 488 | sc-398192 AF488 | 200 µg/ml | $350.00 | |||
CLN3 Antibody (C-1) Alexa Fluor® 546 | sc-398192 AF546 | 200 µg/ml | $350.00 | |||
CLN3 Antibody (C-1) Alexa Fluor® 594 | sc-398192 AF594 | 200 µg/ml | $350.00 | |||
CLN3 Antibody (C-1) Alexa Fluor® 647 | sc-398192 AF647 | 200 µg/ml | $350.00 | |||
CLN3 Antibody (C-1) Alexa Fluor® 680 | sc-398192 AF680 | 200 µg/ml | $350.00 | |||
CLN3 Antibody (C-1) Alexa Fluor® 790 | sc-398192 AF790 | 200 µg/ml | $350.00 | |||
CLN3 (C-1) Neutralizing Peptide | sc-398192 P | 100 µg/0.5 ml | $67.00 |