BCKDHA

Gene Symbol BCKDHA
Entrez Gene 282149
Alt Symbol -
Species Bovine
Gene Type protein-coding
Description branched chain keto acid dehydrogenase E1, alpha polypeptide
Other Description 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial|BCKDE1A|BCKDH E1-alpha|branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease)|branched-chain alpha-keto acid dehydrogenase E1 component alpha chain
Swissprots P11178
Accessions DAA19898 P11178 BC109669 AAI09670 J03759 AAA30595 NM_174506 NP_776931
Function The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). {ECO:0000269|PubMed:283398}.
Subcellular Location Mitochondrion matrix {ECO:0000269|PubMed:283398}.
Tissue Specificity Expressed in kidney (at protein level). {ECO:0000269|PubMed:283398}.
Top Pathways Valine, leucine and isoleucine degradation

Recombinant Bovine 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial(BCKDHA) - CSB-YP002605BO CSB-EP002605BO CSB-BP002605BO CSB-MP002605BO from Cusabio

Category Protein
Source Yeast or E.coli or Baculovirus or Mammalian cell
Species Bovine

2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (BCKDHA), Recombinant Protein - MBS953255 from MyBioSource

Category Protein
Prices $1,170.00, $1,170.00, $1,390.00, $1,390.00, $1,880.00, $1,880.00, $2,345.00, $2,345.00
Sizes 500 µg (E-Coli), 50 µg (Baculovirus), 500 µg (Yeast), 50 µg (Mammalian-Cell), 1 mg (E-Coli), 100 µg (Baculovirus), 1 mg (Yeast), 100 µg (Mammalian-Cell)
Source E Coli or Yeast or Baculovirus or Mammalian Cell
Species Bovine
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