Lysine degradation



ACAT1 - from Human

Gene Symbol ACAT1
Entrez Gene 38
Alt Symbol ACAT, MAT, T2, THIL
Gene Type protein-coding
Description acetyl-CoA acetyltransferase 1

ACAT2 - from Human

Gene Symbol ACAT2
Entrez Gene 39
Alt Symbol -
Gene Type protein-coding
Description acetyl-CoA acetyltransferase 2

ALDH2 - from Human

Gene Symbol ALDH2
Entrez Gene 217
Alt Symbol ALDH-E2, ALDHI, ALDM
Gene Type protein-coding
Description aldehyde dehydrogenase 2 family (mitochondrial)

ALDH1B1 - from Human

Gene Symbol ALDH1B1
Entrez Gene 219
Alt Symbol ALDH5, ALDHX
Gene Type protein-coding
Description aldehyde dehydrogenase 1 family, member B1

ALDH9A1 - from Human

Gene Symbol ALDH9A1
Entrez Gene 223
Alt Symbol ALDH4, ALDH7, ALDH9, E3, TMABADH
Gene Type protein-coding
Description aldehyde dehydrogenase 9 family, member A1

ALDH3A2 - from Human

Gene Symbol ALDH3A2
Entrez Gene 224
Alt Symbol ALDH10, FALDH, SLS
Gene Type protein-coding
Description aldehyde dehydrogenase 3 family, member A2

ALDH7A1 - from Human

Gene Symbol ALDH7A1
Entrez Gene 501
Alt Symbol ATQ1, EPD, PDE
Gene Type protein-coding
Description aldehyde dehydrogenase 7 family, member A1

DLST - from Human

Gene Symbol DLST
Entrez Gene 1743
Alt Symbol DLTS
Gene Type protein-coding
Description dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)

ECHS1 - from Human

Gene Symbol ECHS1
Entrez Gene 1892
Alt Symbol ECHS1D, SCEH
Gene Type protein-coding
Description enoyl CoA hydratase, short chain, 1, mitochondrial

EHHADH - from Human

Gene Symbol EHHADH
Entrez Gene 1962
Alt Symbol ECHD, FRTS3, L-PBE, LBFP, LBP, PBFE
Gene Type protein-coding
Description enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase

GCDH - from Human

Gene Symbol GCDH
Entrez Gene 2639
Alt Symbol ACAD5, GCD
Gene Type protein-coding
Description glutaryl-CoA dehydrogenase

HADHA - from Human

Gene Symbol HADHA
Entrez Gene 3030
Alt Symbol ECHA, GBP, HADH, LCEH, LCHAD, MTPA, TP-ALPHA
Gene Type protein-coding
Description hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit

HADH - from Human

Gene Symbol HADH
Entrez Gene 3033
Alt Symbol HAD, HADH1, HADHSC, HCDH, HHF4, MSCHAD, SCHAD
Gene Type protein-coding
Description hydroxyacyl-CoA dehydrogenase

KMT2A - from Human

Gene Symbol KMT2A
Entrez Gene 4297
Alt Symbol ALL-1, CXXC7, HRX, HTRX1, MLL, MLL/GAS7, MLL1, MLL1A, TET1-MLL, TRX1, WDSTS
Gene Type protein-coding
Description lysine (K)-specific methyltransferase 2A

OGDH - from Human

Gene Symbol OGDH
Entrez Gene 4967
Alt Symbol AKGDH, E1k, OGDC
Gene Type protein-coding
Description oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)

PLOD1 - from Human

Gene Symbol PLOD1
Entrez Gene 5351
Alt Symbol EDS6, LH, LH1, LLH, PLOD
Gene Type protein-coding
Description procollagen-lysine, 2-oxoglutarate 5-dioxygenase 1

PLOD2 - from Human

Gene Symbol PLOD2
Entrez Gene 5352
Alt Symbol BRKS2, LH2, TLH
Gene Type protein-coding
Description procollagen-lysine, 2-oxoglutarate 5-dioxygenase 2

SETMAR - from Human

Gene Symbol SETMAR
Entrez Gene 6419
Alt Symbol HsMar1, METNASE, Mar1
Gene Type protein-coding
Description SET domain and mariner transposase fusion gene

SUV39H1 - from Human

Gene Symbol SUV39H1
Entrez Gene 6839
Alt Symbol H3-K9-HMTase 1, KMT1A, MG44, SUV39H
Gene Type protein-coding
Description suppressor of variegation 3-9 homolog 1 (Drosophila)

WHSC1 - from Human

Gene Symbol WHSC1
Entrez Gene 7468
Alt Symbol MMSET, NSD2, REIIBP, TRX5, WHS
Gene Type protein-coding
Description Wolf-Hirschhorn syndrome candidate 1

KMT2D - from Human

Gene Symbol KMT2D
Entrez Gene 8085
Alt Symbol AAD10, ALR, CAGL114, KABUK1, KMS, MLL2, MLL4, TNRC21
Gene Type protein-coding
Description lysine (K)-specific methyltransferase 2D

BBOX1 - from Human

Gene Symbol BBOX1
Entrez Gene 8424
Alt Symbol BBH, BBOX, G-BBH, gamma-BBH
Gene Type protein-coding
Description butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1

PLOD3 - from Human

Gene Symbol PLOD3
Entrez Gene 8985
Alt Symbol LH3
Gene Type protein-coding
Description procollagen-lysine, 2-oxoglutarate 5-dioxygenase 3

SETD1A - from Human

Gene Symbol SETD1A
Entrez Gene 9739
Alt Symbol KMT2F, Set1, Set1A
Gene Type protein-coding
Description SET domain containing 1A

KMT2B - from Human

Gene Symbol KMT2B
Entrez Gene 9757
Alt Symbol CXXC10, HRX2, MLL1B, MLL2, MLL4, TRX2, WBP-7, WBP7
Gene Type protein-coding
Description lysine (K)-specific methyltransferase 2B
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